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| THE CLINICAL PICTURE |
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| Year : 2017 | Volume
: 4
| Issue : 1 | Page : 52-53 |
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Peri-orbital giant hairy congenital melanocytic ‘divided nevus’ with multiple disseminated satellite nevi
Anup Kumar Tiwary Senior Resident , Ambika Dixit
Department of Dermatology, Venereology and Leprosy, Government Medical College, Haldwani, Uttarakhand, India
| Date of Web Publication | 19-Jun-2017 |
Correspondence Address:
Ambika Dixit
Department of Dermatology, Venereology and Leprosy, Government Medical College, Haldwani, Uttarakhand
India
Anup Kumar Tiwary
Department of Dermatology, Venereology and Leprosy, Government Medical College, Haldwani, Uttarakhand
India
 Source of Support: None, Conflict of Interest: None  | Check |
DOI: 10.4103/2349-5847.208352
How to cite this article:
Tiwary AK, Dixit A. Peri-orbital giant hairy congenital melanocytic ‘divided nevus’ with multiple disseminated satellite nevi. Pigment Int 2017;4:52-3 |
A 9-year-old boy presented with asymptomatic, giant hairy pigmented nevus involving both the eyelids of the right side, the left upper eyelid, the right cheek, the nose and the forehead along with multiple, non-hairy, bluish-black, discrete satellite nevi as macules and plaques ranging in size from 0.5 cm × 0.5 cm to 2.0 cm × 1.5 cm over his chest, his back and the upper limbs [Figure 1]. These lesions were present since birth and increasing in size proportionate to his body. Biopsy taken from the pigmented plaque type lesion was consistent with compound melanocytic nevus [Figure 2]. The rest of the mucocutaneous sites were normal. Eye movements and refraction testing were also unremarkable, but fundoscopy, computed tomography and magnetic resonance imaging imaging could not be performed for any ophthalmic and neural associations due to the denial of the parents. | Figure 1: (a) Giant hairy melanocytic nevus involving both the eyelids of the right side, the left upper eyelid, the right cheek, the nose and the forehead; (b)–(d) multiple, bluish-black, satellite nevi over his chest, his back and the upper limbs
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 | Figure 2: Proliferative dermal nodule consisting of larger, pigmented nevus cells of epithelioid shape scattered and in the form of nests at the dermo-epidermal junction and the upper dermis (haematoxylin and eosin, ×400)
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Giant congenital melanocytic nevus (GCMN) is usually defined as a melanocytic lesion with a maximum diameter of ≥20 cm, present since birth, with an incidence of <1 in 20,000 live births.[1] To the best of our knowledge, the Peri-orbital distribution along with both eyelids involvement (as seen in our case) has been rarely reported entity in the English medical literature.[2] A similar case was reported in a 6-year-old girl with peri-orbital GCMN and conjunctival melanosis.[1] The other prominent finding in our case of ‘multiple satellite nevi’ increases the risk of neurocutaneous melanosis and malignant melanoma.[3]
Declaration of patient consent
The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.
Financial support and sponsorship
Nil.
Conflicts of interest
There are no conflicts of interest.
| References | |  |
| 1. | Raina UK, Seth A, Gupta A, Batta S. Ocular findings in a case of periorbital giant congenital melanocytic nevus. Oman J Ophthalmol 2014;7:153-5.  [ PUBMED] [Full text] |
| 2. | Margulis A, Adler N, Bauer BS. Congenital melanocytic nevi of the eyelids and periorbital region. Plast Reconstr Surg 2009;124:1273-83. [ PUBMED] |
| 3. | Marghoob AA, Dusza S, Oliveria S, Halpern AC. Number of satellite nevi as a correlate for neurocutaneous melanocytosis in patients with large congenital melanocytic nevi. Arch Dermatol 2004;140:171-5. [ PUBMED] |
[Figure 1], [Figure 2]
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